Recombinant Human Sterol carrier protein 2 (ab117049)

製品の概要

  • 製品名Recombinant Human Sterol carrier protein 2
  • タンパク質長Full length protein

製品の詳細

  • 由来Recombinant
  • 由来Wheat germ
  • アミノ酸配列
    • アクセッション番号P22307-2
    • 生物種Human
    • 配列MGFPEAASSFRTHQIEAVPTSSASDGFKANLVFKEIEKKLEEEGEQFVKK IGGIFAFKVKDGPGGKEATWVVDVKNGKGSVLPNSDKKADCTITMADSDF LALMTGKMNPQSAFFQGKLKITGNMGLAMKLQNLQLQPGNAKL
    • 分子量42 kDa including tags
    • 領域1 to 143

特性

Our Abpromise guarantee covers the use of ab117049 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

  • アプリケーション

    Western blot

    ELISA

    SDS-PAGE

  • 製品の状態Liquid
  • 備考Protein concentration is above or equal to 0.05 mg/ml.
    Best used within three months from the date of receipt.
  • Concentration information loading...

前処理および保存

  • 保存方法および安定性

    Shipped on dry ice. Upon delivery aliquot and store at -80ºC. Avoid freeze / thaw cycles.

    pH: 8.00
    Constituents: 0.3% Glutathione, 0.79% Tris HCl

関連情報

  • 別名
    • DKFZp686C12188
    • DKFZp686D11188
    • NLTP
    • NLTP_HUMAN
    • Non-specific lipid-transfer protein
    • Nonspecific lipid transfer protein
    • NSL TP
    • NSL-TP
    • OTTHUMP00000010488
    • OTTHUMP00000231766
    • OTTHUMP00000231767
    • OTTHUMP00000231768
    • OTTHUMP00000231769
    • OTTHUMP00000231770
    • OTTHUMP00000231772
    • OTTHUMP00000231773
    • OTTHUMP00000231774
    • OTTHUMP00000231776
    • OTTHUMP00000234662
    • Propanoyl CoA C acyltransferase
    • Propanoyl-CoA C-acyltransferase
    • SCP 2
    • SCP chi
    • SCP X
    • SCP-2
    • SCP-chi
    • SCP-X
    • SCP2
    • SCPchi
    • SCPX
    • Sterol carrier protein 2
    • Sterol carrier protein X
    see all
  • 機能Mediates in vitro the transfer of all common phospholipids, cholesterol and gangliosides between membranes. May play a role in regulating steroidogenesis.
  • 組織特異性Liver, fibroblasts, and placenta.
  • 関連疾患Defects in SCP2 are a cause of leukoencephalopathy with dystonia and motor neuropathy (LDMN) [MIM:613724]; also known as sterol carrier protein 2 deficiency. LDMN is a syndrome characterized by leukoencephalopathy, dystonic head tremor, spasmodic torticollis and reduced tendon reflexes in lower extremities. Additional features include hyposmia, pathologic saccadic eye movements, a slight hypoacusis, accumulation of branched-chain pristanic acid in plasma, and the presence of abnormal bile alcohol glucuronides in urine.
  • 配列類似性In the N-terminal section; belongs to the thiolase family.
    Contains 1 SCP2 domain.
  • 細胞内局在Mitochondrion; Cytoplasm. Mitochondrion. Cytoplasmic in the liver and also associated with mitochondria especially in steroidogenic tissues and Peroxisome. Interaction with PEX5 is essential for peroxisomal import.
  • Information by UniProt

Recombinant Human Sterol carrier protein 2 画像

  • 12.5% SDS-PAGE showing ab117049 at approximately 41.84 kDa.
    Stained with Coomassie Blue.

Recombinant Human Sterol carrier protein 2 (ab117049) 使用論文

ab117049 has not yet been referenced specifically in any publications.

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Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"