Naseri NN et al.Novel Metabolic Abnormalities in the Tricarboxylic Acid Cycle in Peripheral Cells From Huntington's Disease Patients.PLoS One 11:e0160384 (2016).
Ferriero R et al.Phenylbutyrate therapy for pyruvate dehydrogenase complex deficiency and lactic acidosis.Sci Transl Med 5:175ra31 (2013).
Donohoe DR et al.Microbial regulation of glucose metabolism and cell-cycle progression in Mammalian colonocytes.PLoS One 7:e46589 (2012).
Elrod JW et al.Cyclophilin D controls mitochondrial pore-dependent Ca(2+) exchange, metabolic flexibility, and propensity for heart failure in mice.J Clin Invest 120:3680-7 (2010).
Martinez-Outschoorn UE et al.Oxidative stress in cancer associated fibroblasts drives tumor-stroma co-evolution: A new paradigm for understanding tumor metabolism, the field effect and genomic instability in cancer cells.Cell Cycle 9:3256-76 (2010).
Quintana E et al.PDH E(1)beta deficiency with novel mutations in two patients with Leigh syndrome.J Inherit Metab Dis : (2009).
Bonnet S et al.A mitochondria-K+ channel axis is suppressed in cancer and its normalization promotes apoptosis and inhibits cancer growth.Cancer Cell 11:37-51 (2007).
Richards EM et al.Postischemic hyperoxia reduces hippocampal pyruvate dehydrogenase activity.Free Radic Biol Med 40:1960-70 (2006).