製品の概要

  • 製品名Anti-PEX13 antibody
    PEX13 一次抗体 製品一覧
  • 製品の詳細
    Rabbit polyclonal to PEX13
  • アプリケーション適用あり: WBmore details
  • 種交差性
    交差種: Human
  • 免疫原

    Synthetic peptide, corresponding to a sequence within amino acids 342 - 403 of Human PEX13.

  • ポジティブ・コントロール
    • MOLT4 whole cell lysate.

法規制情報

製品の特性

関連製品

アプリケーション

Our Abpromise guarantee covers the use of ab96841 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

アプリケーション Abreviews 特記事項
WB 1/500 - 1/3000. Predicted molecular weight: 44 kDa.

ターゲット情報

  • 機能Component of the peroxisomal translocation machinery with PEX14 and PEX17. Functions as a docking factor for the predominantly cytoplasmic PTS1 receptor (PAS10/PEX5). Involved in the import of PTS1 and PTS2 proteins.
  • 関連疾患Defects in PEX13 are the cause of peroxisome biogenesis disorder complementation group 13 (PBD-CG13) [MIM:601789]; also known as PBD-CGH. PBD-CG13 is a peroxisomal disorder arising from a failure of protein import into the peroxisomal membrane or matrix. The peroxisome biogenesis disorders (PBD group) are genetically heterogeneous with at least 14 distinct genetic groups as concluded from complementation studies. Include disorders are: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). ZWS, NALD and IRD are distinct from RCDP and constitute a clinical continuum of overlapping phenotypes known as the Zellweger spectrum (PBD-ZSS).
    Defects in PEX13 are a cause of adrenoleukodystrophy neonatal (NALD) [MIM:202370]. NALD is a peroxisome biogenesis disorder (PBD) characterized by the accumulation of very long-chain fatty acids, adrenal insufficiency and mental retardation.
  • 配列類似性Belongs to the peroxin-13 family.
    Contains 1 SH3 domain.
  • 細胞内局在Peroxisome membrane.
  • Information by UniProt
  • 参照データベース
  • 別名
    • 2610008O20Rik antibody
    • NALD antibody
    • OTTMUSP00000005454 antibody
    • Peroxin 13 antibody
    • Peroxin-13 antibody
    • Peroxin13 antibody
    • Peroxisomal membrane protein PEX 13 antibody
    • Peroxisomal membrane protein PEX13 antibody
    • Peroxisome biogenesis factor 13 antibody
    • PEX 13 antibody
    • pex13 antibody
    • PEX13_HUMAN antibody
    • RP23-188K3.1 antibody
    • ZWS antibody
    see all

Anti-PEX13 antibody 画像

  • Anti-PEX13 antibody (ab96841) at 1/1000 dilution + MOLT4 whole cell lysate at 30 µg

    Predicted band size : 44 kDa

Anti-PEX13 antibody (ab96841) 使用論文

ab96841 has not yet been referenced specifically in any publications.

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Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"