製品の概要

  • 製品名
  • 製品の詳細
    Mouse polyclonal to PDSS2
  • アプリケーション
    適用あり: WBmore details
  • 種交差性
    交差種: Human
  • 免疫原

    Full-length Human PDSS2 (NP_065114)

  • ポジティブ・コントロール
    • Human kidney tissue

製品の特性

アプリケーション

Our Abpromise guarantee covers the use of ab88817 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

アプリケーション Abreviews 特記事項
WB 1/500 - 1/1000. Predicted molecular weight: 44 kDa.

ターゲット情報

  • 機能
    Supplies decaprenyl diphosphate, the precursor for the side chain of the isoprenoid quinones ubiquinone-10.
  • パスウェイ
    Cofactor biosynthesis; ubiquinone biosynthesis.
  • 関連疾患
    Defects in PDSS2 are a cause of coenzyme Q10 deficiency (COQ10D) [MIM:607426]. Coenzyme Q10 deficiency is an autosomal recessive disorder with variable manifestations. It can be associated with three main clinical phenotypes: a predominantly myopathic form with central nervous system involvement, an infantile encephalomyopathy with renal dysfunction and an ataxic form with cerebellar atrophy.
  • 配列類似性
    Belongs to the FPP/GGPP synthase family.
  • 細胞内局在
    Mitochondrion.
  • Information by UniProt
  • 参照データベース
  • 別名
    • All-trans-decaprenyl-diphosphate synthase subunit 2 antibody
    • bA59I9.3 antibody
    • C6orf210 antibody
    • Candidate tumor suppressor protein antibody
    • chromosome 6 open reading frame 210 antibody
    • Decaprenyl pyrophosphate synthase subunit 2 antibody
    • decaprenyl pyrophosphate synthetase subunit 2 antibody
    • Decaprenyl-diphosphate synthase subunit 2 antibody
    • DLP1 antibody
    • DLP1_HUMAN antibody
    • hDLP1 antibody
    • Pdss2 antibody
    • prenyl (decaprenyl) diphosphate synthase, subunit 2 antibody
    • subunit 2 of decaprenyl diphosphate synthase antibody
    see all

画像

  • Anti-PDSS2 antibody (ab88817) at 1/500 dilution + Human kidney tissue lysate at 50 µg

    Predicted band size : 44 kDa
    Observed band size : 44 kDa
  • All lanes : Anti-PDSS2 antibody (ab88817) at 1/500 dilution

    Lane 1 : transfected 293T cell lysate
    Lane 2 : untransfected 293T cell lysate

    Lysates/proteins at 25 µg per lane.


    Predicted band size : 44 kDa
    Observed band size : 44 kDa

プロトコール

参考文献

ab88817 has not yet been referenced specifically in any publications.

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Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"

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