製品の概要

製品の詳細

  • 由来
    Synthetic
  • アミノ酸配列
    • 生物種
      Human
    • 配列
      TILTYPFKNLPT-C
    • 領域
      2 to 13

関連製品

特性

Our Abpromise guarantee covers the use of ab23180 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

  • アプリケーション

    Blocking - Blocking peptide for Anti-HADHB antibody (ab10093)

  • 製品の状態
    Liquid
  • Concentration information loading...

前処理および保存

  • 保存方法および安定性

    Shipped at 4°C. Upon delivery aliquot and store at -20°C or -80°C. Avoid repeated freeze / thaw cycles.

関連情報

  • 別名
    • 2 enoyl Coenzyme A (CoA) hydratase beta subunit
    • 3 ketoacyl Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein beta subunit
    • 3 ketoacyl Coenzyme A thiolase
    • 3 ketoacyl Coenzyme A thiolase of mitochondrial trifunctional protein beta subunit
    • 3-ketoacyl-CoA thiolase
    • Acetyl CoA acyltransferase
    • Acetyl-CoA acyltransferase
    • Beta ketothiolase
    • Beta-ketothiolase
    • ECHB
    • ECHB_HUMAN
    • HADH
    • Hadhb
    • Hydroxyacyl CoA dehydrogenase/3 ketoacyl CoA thiolase/enoyl CoA hydratase (trifunctional protein), beta subunit
    • Hydroxyacyl Coenzyme A (CoA) dehydrogenase beta subunit
    • Hydroxyacyl Coenzyme A dehydrogenase
    • Hydroxyacyl Coenzyme A dehydrogenase beta subunit
    • Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) beta subunit
    • MGC87480
    • Mitochondrial trifunctional enzyme beta subunit
    • Mitochondrial trifunctional protein beta subunit
    • MSTP 029
    • MSTP029
    • MTPB
    • TP beta
    • TP-beta
    • TPbeta
    • Trifunctional enzyme subunit beta
    • Trifunctional enzyme subunit beta mitochondrial
    • Trifunctional protein
    see all
  • パスウェイ
    Lipid metabolism; fatty acid beta-oxidation.
  • 関連疾患
    Defects in HADHB are a cause of trifunctional protein deficiency (TFP deficiency) [MIM:609015]. The clinical manifestations are very variable and include hypoglycemia, cardiomyopathy and sudden death. Phenotypes with mainly hepatic and neuromyopathic involvement can also be distinguished. Biochemically, TFP deficiency is defined by the loss of all three enzyme activities of the TFP complex.
  • 配列類似性
    Belongs to the thiolase family.
  • 細胞内局在
    Mitochondrion.
  • Information by UniProt

Human HADHB peptide (ab23180) 使用論文

ab23180 has not yet been referenced specifically in any publications.

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Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"

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