製品の概要

  • 製品名Anti-HPS6 antibody
    HPS6 一次抗体 製品一覧
  • 製品の詳細
    Rabbit polyclonal to HPS6
  • アプリケーション適用あり: WBmore details
  • 種交差性
    交差種: Human
  • 免疫原

    Amino acids 405-466 of Human HPS6 (NP_079023)

    EEACGYYQRRSLRGAQLTPEELRHSSTFRAPQALASILQGHLPPSALLTM LRTELRDYRGLE

  • ポジティブ・コントロール
    • H1299, HeLa and HepG2 cell lines. A431 whole cell lysate.

法規制情報

製品の特性

  • 製品の状態Liquid
  • 保存方法Shipped at 4°C. Upon delivery aliquot. Store at -20°C or -80°C. Avoid freeze / thaw cycle.
  • バッファーPreservative: 0.01% Thimerosal (merthiolate)
    Constituents: 10% Glycerol, 0.1M Tris, 0.1M Glycine, pH 7.0
  • Concentration information loading...
  • 精製度Immunogen affinity purified
  • ポリ/モノポリクローナル
  • アイソタイプIgG
  • 研究分野

関連製品

アプリケーション

Our Abpromise guarantee covers the use of ab96656 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

アプリケーション Abreviews 特記事項
WB 1/1000. Predicted molecular weight: 83 kDa.

ターゲット情報

  • 機能May regulate the synthesis and function of lysosomes and of highly specialized organelles, such as melanosomes and platelet dense granules.
  • 組織特異性Ubiquitous.
  • 関連疾患Defects in HPS6 are the cause of Hermansky-Pudlak syndrome type 6 (HPS6) [MIM:614075]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.
  • 細胞内局在Microsome membrane. Cytoplasm > cytosol. Early endosome membrane.
  • Information by UniProt
  • 参照データベース
  • 別名
    • FLJ22501 antibody
    • Hermansky Pudlak syndrome 6 protein antibody
    • Hermansky-Pudlak syndrome 6 protein antibody
    • HPS6 antibody
    • HPS6_HUMAN antibody
    • MGC20522 antibody
    • Ru antibody
    • Ruby eye protein homolog antibody
    • Ruby-eye protein homolog antibody
    see all

Anti-HPS6 antibody 画像

  • Anti-HPS6 antibody (ab96656) at 1/1000 dilution + A431 whole cell lysate at 30 µg

    Predicted band size : 83 kDa

Anti-HPS6 antibody (ab96656) 使用論文

ab96656 has not yet been referenced specifically in any publications.

Product Wall

There are currently no Abreviews or Questions for ab96656.
Please use the links above to contact us or submit feedback about this product.

Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"