Anti-Fumarylacetoacetate hydrolase 抗体 [2] (ab83078)

製品の概要

  • 製品名Anti-Fumarylacetoacetate hydrolase antibody [2]
    Fumarylacetoacetate hydrolase 一次抗体 製品一覧
  • 製品の詳細
    Mouse monoclonal [2] to Fumarylacetoacetate hydrolase
  • アプリケーション適用あり: WB, ELISAmore details
  • 種交差性
    交差種: Human
  • 免疫原

    Recombinant full length Human Fumarylacetoacetate hydrolase protein expressed in E. coli.

  • ポジティブ・コントロール
    • HEK293 whole cell lysate

製品の特性

関連製品

アプリケーション

Our Abpromise guarantee covers the use of ab83078 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

アプリケーション Abreviews 特記事項
WB 1/1000. Predicted molecular weight: 46 kDa.
ELISA Use at an assay dependent dilution.

ターゲット情報

  • 関連性Fumarylacetoacetate hydrolase is the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). This is an autosomal recessive inborn error of metabolism that occurs in both an acute and a chronic form. Clinical characteristics of the acute form include hepatic failure and death in infancy, whereas children with the chronic form have renal tubular dysfunction and hypophosphatemic rickets, progressive liver disease with development of hepatocellular carcinoma. Dietary treatment with restriction of tyrosine and phenylalanine alleviates the rickets, but liver transplantation has so far been the only definite treatment.
  • 参照データベース
  • 別名
    • Beta diketonase antibody
    • FAA antibody
    • FAH antibody
    • Fumarylacetoacetase antibody
    • Fumarylacetoacetate antibody
    • Fumarylacetoacetate hydrolase antibody
    see all

Anti-Fumarylacetoacetate hydrolase antibody [2] 画像

  • Anti-Fumarylacetoacetate hydrolase antibody [2] (ab83078) at 1/500 dilution + Whole cell lysates prepared from HEK293 cells.

    Predicted band size : 46 kDa

Anti-Fumarylacetoacetate hydrolase antibody [2] (ab83078) 使用論文

ab83078 has not yet been referenced specifically in any publications.

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