製品の概要

  • 製品名
  • 製品の詳細
    Goat polyclonal to ETFDH
  • アプリケーション
    適用あり: WBmore details
  • 種交差性
    交差種: Mouse, Rat, Human
    交差が予測される動物種: Rabbit, Cow, Dog, Pig, Zebrafish, Orangutan
  • 免疫原

    Synthetic peptide:

    C-EHDQPAHLTLRD

    , corresponding to internal sequence amino acids 530-541 of Human ETFDH (NP_004444.2).

  • ポジティブ・コントロール
    • Human, Mouse and Rat Heart lysates, Human kidney lysate.

製品の特性

アプリケーション

Our Abpromise guarantee covers the use of ab103910 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

アプリケーション Abreviews 特記事項
WB Use a concentration of 1 - 3 µg/ml. Predicted molecular weight: 69 kDa.

ターゲット情報

  • 機能
    Accepts electrons from ETF and reduces ubiquinone.
  • 関連疾患
    Defects in ETFDH are the cause of glutaric aciduria type 2C (GA2C) [MIM:231680]. GA2C is an autosomal recessively inherited disorder of fatty acid, amino acid, and choline metabolism. It is characterized by multiple acyl-CoA dehydrogenase deficiencies resulting in large excretion not only of glutaric acid, but also of lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids.
  • 配列類似性
    Belongs to the ETF-QO/fixC family.
    Contains 1 4Fe-4S ferredoxin-type domain.
  • 細胞内局在
    Mitochondrion inner membrane.
  • Information by UniProt
  • 参照データベース
  • 別名
    • Electron transfer flavoprotein ubiquinone oxidoreductase antibody
    • Electron transfer flavoprotein-ubiquinone oxidoreductase antibody
    • electron transferring flavoprotein dehydrogenase antibody
    • Electron-transferring-flavoprotein dehydrogenase antibody
    • ETF dehydrogenase antibody
    • ETF QO antibody
    • ETF ubiquinone oxidoreductase antibody
    • ETF-QO antibody
    • ETF-ubiquinone oxidoreductase antibody
    • ETFD_HUMAN antibody
    • Etfdh antibody
    • MADD antibody
    • mitochondrial antibody
    see all

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プロトコール

参考文献

ab103910 has not yet been referenced specifically in any publications.

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Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"

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