製品の概要

  • 製品名
  • 製品の詳細
    Rabbit polyclonal to BCKDHB
  • アプリケーション
    適用あり: WBmore details
  • 種交差性
    交差種: Human
  • 免疫原

    Synthetic peptide conjugated to KLH, corresponding to a region within N terminal amino acids 44-74 of Human BCKDHB (NP_000047.1).

  • ポジティブ・コントロール
    • HeLa cell line lysate

製品の特性

アプリケーション

Our Abpromise guarantee covers the use of ab107398 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

アプリケーション Abreviews 特記事項
WB 1/100 - 1/500. Predicted molecular weight: 43 kDa.

ターゲット情報

  • 機能
    The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3).
  • 関連疾患
    Defects in BCKDHB are the cause of maple syrup urine disease type IB (MSUD1B) [MIM:248600]. MSUD is an autosomal recessive disorder characterized by mental and physical retardation, feeding problems, and a maple syrup odor to the urine.
  • 細胞内局在
    Mitochondrion matrix.
  • Information by UniProt
  • 参照データベース
  • 別名
    • 2 oxoisovalerate dehydrogenase subunit beta mitochondrial antibody
    • 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial antibody
    • BCKDE1B antibody
    • BCKDH E1-beta antibody
    • BCKDHB antibody
    • Branched chain alpha ketoacid dehydrogenase E1 beta subunit antibody
    • Branched chain keto acid dehydrogenase E1 beta polypeptide antibody
    • Branched-chain alpha-keto acid dehydrogenase E1 component beta chain antibody
    • dJ279A18.1 antibody
    • E1B antibody
    • E1b beta subunit of the branched chain complex antibody
    • FLJ17880 antibody
    • ODBB_HUMAN antibody
    • RP1-279A18.1 antibody
    see all

画像

  • Anti-BCKDHB antibody (ab107398) at 1/100 dilution + HeLa cell line lysate at 35 µg

    Predicted band size : 43 kDa

プロトコール

参考文献

ab107398 has not yet been referenced specifically in any publications.

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Please note: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"

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