製品の概要

  • 製品名Anti-ATPAF2 antibody
    ATPAF2 一次抗体 製品一覧
  • 製品の詳細
    Rabbit polyclonal to ATPAF2
  • 特異性This antibody detects endogenous levels of total ATPAF2 protein.
  • アプリケーション適用あり: ELISA, WBmore details
  • 種交差性
    交差種: Human
    交差が予測される動物種: Mouse
  • 免疫原

    A synthesized peptide derived from the internal region of human ATPAF2.

  • ポジティブ・コントロール
    • Extracts from Jurkat cells.

製品の特性

アプリケーション

Our Abpromise guarantee covers the use of ab74235 in the following tested applications.

The application notes include recommended starting dilutions; optimal dilutions/concentrations should be determined by the end user.

アプリケーション Abreviews 特記事項
ELISA 1/40000.
WB 1/500 - 1/1000. Detects a band of approximately 33 kDa (predicted molecular weight: 33 kDa).

ターゲット情報

  • 関連性ATPAF2 belongs to the ATP12 family. It may play a role in the assembly of the F1 component of the mitochondrial ATP synthase (ATPase). Defects in ATPAF2 are the cause of complex V mitochondrial respiratory chain ATPAF2 subunit deficiency (ATPAF2 deficiency) [MIM:604273]; also called ATP synthase deficiency or ATPase deficiency. ATPAF2 deficiency seems to be an early presenting disease in which lactic acidosis, dysmorphic features, and methyl glutaconic aciduria can be major clues in the diagnosis. Dysmorphic features include a large mouth, prominent nasal bridge, micrognathia, rocker-bottom feet and flexion contractures of the limbs associated with camptodactyly. Patients are hypertonic and have an enlarged liver, hypoplastic kidneys and elevated lactate levels in urine, plasma and cerebro spinal fluid (CSF).
  • 細胞内局在Mitochondrion
  • 参照データベース
  • 別名
    • ATP synthase mitochondrial F1 complex assembly factor 2 antibody
    • ATP12 antibody
    • ATP12 homolog antibody
    • ATP12p antibody
    • LP3663 antibody
    see all

Anti-ATPAF2 antibody 画像

  • All lanes : Anti-ATPAF2 antibody (ab74235) at 1/500 dilution

    Lane 1 : Extracts from Jurkat cells
    Lane 2 : Extracts from Jurkat cells plus 5µg immunizing peptide

    Lysates/proteins at 5 µg per lane.


    Predicted band size : 33 kDa
    Observed band size : 33 kDa

Anti-ATPAF2 antibody (ab74235) 使用論文

ab74235 has not yet been referenced specifically in any publications.

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